Objective: To study the diagnostic and prognostic value of prenatal ultrasound inspection on fetal Dandy-Walker syndrome. Methods:Ultrasound images, ultrasonic reexamination results and follow-up results of 27 fetuses who were diagnosed with Dandy-walker syndrome in our hospital from august 2017 to august 2021 were collected and analyzed. Results: Twenty seven fetuses with Dandy-Walker syndrome were selected, including 8 cases of Dandy-Walker malformation, 7 cases of Dandy-walker variant, 12 cases of simple dilatation of the posterior fossa cistern.Thirteen cases in the 27 fetus were detected with malformation such as hydrocephalus, malformations of cleft lip and palate, cardiovascular abnormalities, skeletal musculature system and urinary tract were also found. Combined ultrasonographic soft makers such as enlarged lateral ventricles (diameter between 10mm and 15mm), slight renal pelvis dilation, single umbilical artery and cavum vergae were found. Two cases of Dandy -Walker variants were aneuploidy. Most pregnant women choose to terminate pregnancy after being diagnosed with Dandy-Walker syndrome combining deformity or variant. Fetuses with simple dilatation of the posterior fossa cistern had good prognosis. Conclusion: Prenatal ultrasound inspection on fetal Dandy-Walker syndrome is of great clinical value. Dandy-Walker malformation and variant fetal with malformation is of diversity and multiplicity and closely related with multiploid. Fetuses with simple dilatation of the posterior fossa cistern usually have good prognosis.
BAI Yan
,
LI Aihua
. Clinical analysis of fetal Dandy-Walker syndrome with malformation and obstetric outcomes[J]. Journal of Baotou Medical College, 2023
, 39(7)
: 25
-28
.
DOI: 10.16833/j.cnki.jbmc.2023.07.005
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